What is Supravalvular mitral ring?

The supravalvular mitral ring is a ridge or membrane arising from the left atrial wall overlying the mitral valve and is sometimes attached to the mitral valve anulus, variable in thickness and extension it can range from being a thin membrane to a thick fibrous ridge.

What is Lutembacher syndrome?

Lutembacher’s syndrome refers to a congenital atrial septal defect (ASD) complicated by acquired mitral stenosis (MS). [1] It comprises of Atrial Septal Defect (ASD) [Ostium Secundum] with Mitral stenosis (MS). Inter-atrial septum develops from two sources-septum primium and septum secundum.

What is shone’s disease?

Shone’s syndrome (also known as Shone’s complex) is a rare combination of four left-sided congenital cardiac anomalies including parachute mitral valve, supravalvar mitral ring, coarctation (narrowing) of the aor- ta, and subaortic obstruction.

What type of murmur is mitral stenosis?

The diastolic murmur of mitral stenosis is of low pitch, rumbling in character, and best heard at the apex with the patient in the left lateral position. It commences after the opening snap of the mitral valve, and the duration of the murmur correlates with the severity of the stenosis.

How does an annuloplasty ring work?

In an annuloplasty, the doctor measures the size of the existing ring. Then the doctor sews a band to the existing ring around the valve. The band may be rigid or flexible. This procedure can be done during open-heart surgery or minimally invasive heart surgery, which involves smaller incisions.

Does mitral valve stenosis cause pulmonary hypertension?

Like other heart valve problems, mitral valve stenosis can strain your heart and decrease blood flow. Untreated, mitral valve stenosis can lead to complications such as: High blood pressure in the lung arteries (pulmonary hypertension).

What causes an opening snap?

An opening snap occurring early in diastole along with a single second heart sound can mimic a split second heart sound. An opening snap is caused by thickened valve leaflets. When they open it produces a snapping sound. The more severe the thickening the earlier in diastole the opening snap occurs.

Is Shone syndrome genetic?

The team found that mutations in the gene encoding myosin, a contractile protein that is highly expressed during development accounted for about 11 percent of Shone syndrome. The team also reports a shared mutation among some CHD patients with Ashkenazian ancestry.

What is a Konno procedure?

The Ross-Konno procedure is an open-heart surgery done under general anesthesia and cardiopulmonary bypass. It involves removing the damaged aortic valve, removing the pulmonary valve, and putting the pulmonary valve in place of the damaged aortic valve.

What is the best way to hear mitral stenosis?

Mitral stenosis Best heard as the patient is rolled onto left side with stethoscope bell at apex. Better heard after exercise.

What is life expectancy after mitral valve repair?

Median survival after MV ‐repair was 7.8 years, close to 8.5 years (95% CI : 8.2–9.4) in the age‐matched UK population (ratio 0.9). Rate of re‐operation for MV ‐dysfunction was 2.3% versus 2.5% (mitral valve replacement, P=1.0).