What is cerebral Hemiatrophy?

Cerebral hemiatrophy, a disease of childhood, is characterised clinically by seizures, hemiparesis and mental retardation.[1,2] Dyke, Davidoff, and Masson, in 1933, described the plain skull radiographic and pneumoecephalographic changes, in a series of nine patients, characterized by hemiparesis, seizures, facial- …

What causes Hemiatrophy?

Hemidystonia-hemiatrophy (HD-HA) is a rare dystonia, usually caused by a static cerebral injury occurring at birth or during infancy, that is characterized by a combination of hemidystonia (HD), involving one half of the body, and hemiatrophy (HA) on the same side as the HD.

What is Hemiatrophy?

: atrophy that affects one half of an organ or part or one side of the whole body facial hemiatrophy — compare hemihypertrophy.

What is Dyke Davidson Masson syndrome?

Dyke-Davidoff-Masson syndrome is a condition characterized by hemicerebral atrophy/hypoplasia secondary to brain insult usually in fetal or early childhood period and is accompanied by ipsilateral compensatory osseous hypertrophy and contralateral hemiparesis.

What is diffuse cerebral atrophy?

Overview. Brain atrophy — or cerebral atrophy — is the loss of brain cells called neurons. Atrophy also destroys the connections that help the cells communicate. It can be a result of many different diseases that damage the brain, including stroke and Alzheimer’s disease.

What is Romberg’s disease?

Parry-Romberg syndrome is a rare disorder characterized by slowly progressive deterioration (atrophy) of the skin and soft tissues of half of the face (hemifacial atrophy), usually the left side.

What causes Hemimegalencephaly?

Hemimegalencephaly is caused by a spontaneous mutation which occurs on the mTOR pathway at approximately the third week of gestation. It is genetic (meaning that it involves genes) but is not hereditary. There are no reported cases of two or more children with hemimegalencephaly in one family.

How does cerebral hemiatrophy syndrome affect the brain?

Cerebral hemiatrophy syndromes are uncommon disorders resulting in atrophy or hypoplasia of one cerebral hemisphere. In adults, cerebral hemiatrophy is also characterized by unilateral brain volume loss, however without these compensatory osseous changes.

What is the difference between hemiparkinsonism and hemiatrophy syndrome?

Hemiparkinsonism with hemiatrophy syndrome is defined by the occurrence of a body hemiatrophy with features of an early onset, slowly progressive, asymmetric parkinsonism more prominent on the side of the hemiatrophy. The underlying pathogenesis is not well understood but perinatal cerebral insults seem to play a crucial role.

Which is the best reference for cerebral hemiatrophy?

Oyama N, Terae S, Saitoh S et-al. Bilateral germinoma involving the basal ganglia and cerebral white matter. AJNR Am J Neuroradiol. 2005;26 (5): 1166-9.

Which is an uncommon condition characterized by hemidystonia and hemiatrophy?

Hemidystonia-hemiatrophy syndrome (HD-HA) is an uncommon condition characterized by hemidystonia and hemiatrophy. In one study, hemiparesis preceded HD in 88% of HDHA cases ( Wijemanne and Jankovic, 2009 ).