What is meant by hypsarrhythmia?
Definition. Hypsarrhythmia is abnormal interictal high amplitude waves and a background of irregular spikes. There is continuous (during wakefulness), high-amplitude (>200 Hz), generalized polymorphic slowing with no organized background and multifocal spikes demonstrated by electroencephalography (EEG). [
How do I know if I have hypsarrhythmia?
It is an abnormal interictal pattern, consisting of high amplitude and irregular waves and spikes in a background of chaotic and disorganized activity seen on electroencephalogram (EEG), and frequently encountered in infants diagnosed with infantile spasms, although it can be found in other conditions.
What does hypsarrhythmia look like on EEG?
The term hypsarrhythmia in an EEG report is specific for a diagnosis of infantile spasms. The hypsarrhythmic EEG pattern is a high-amplitude, chaotic slowing of generalized distribution without interhemispheric synchronization and with multifocal epileptiform discharges throughout.
How do you get rid of hypsarrhythmia?
Get rid of hypsarrhythmia — the abnormal chaotic brainwave pattern….If your child doesn’t respond to either hormone treatments or vigabatrin, further treatment options include:
- The ketogenic diet.
- Other anti-seizure medicine.
- Surgery.
Does West syndrome go away?
West syndrome (also called infantile spasms) should go away by the time your child is 4 years old. But most people will develop another kind of epilepsy or seizure condition in childhood or as an adult. About 1 in 5 will have Lennox-Gastaut syndrome, a severe form of epilepsy with multiple types of seizures.
What is West syndrome?
West syndrome is a constellation of symptoms characterized by epileptic/infantile spasms, abnormal brain wave patterns called hypsarrhythmia and intellectual disability.
Is West syndrome fatal?
It’s rare, but some children who had West syndrome as babies will die before adulthood. It usually happens before the age of 10.
Is West syndrome a rare disease?
West syndrome is a rare neurological syndrome that can affect males and females. The X-linked form of West syndrome affects males more often than females. West syndrome has been estimated to affect . 31 per 1000 live births in the United States.
What is Doose Syndrome?
Myoclonic astatic epilepsy (MAE), also known as Doose syndrome, is an epilepsy syndrome of early childhood, most commonly appearing between ages 1 and 5 and featuring generalized seizures. Children will experience drop attacks and staring seizures, sometimes associated with falls.
Can you live a normal life with West syndrome?
West syndrome is generally not life-threatening but it occurs more often in children with life-threatening conditions. Furthermore, the treatments used for West syndrome can (rarely) cause death. As a result, only 5 out of every 100 children diagnosed with West syndrome will not survive beyond the age of five years.
How many variants of hypsarrhythmia have been identified?
Through the use of video EEG and continuous monitoring, five variants of the “classical” hypsarrhythmic pattern have been identified: Hypsarrhythmia with increased interhemispheric synchronization.
What does hypsarrhythmia stand for in West syndrome?
Classification. Hypsarrhythmia with little spike or sharp activity. The “H” in PEHO syndrome stands for hypsarrhythmia. Together with developmental regression and infantile spasms, hypsarrhythmia is one of the diagnostic criteria for West syndrome.
What does it mean when an infant has hypsarrhythmia?
Hypsarrhythmia. It is an abnormal interictal pattern, consisting of high amplitude and irregular waves and spikes in a background of chaotic and disorganized activity seen on electroencephalogram (EEG), and frequently encountered in an infant diagnosed with infantile spasms, although it can be found in other conditions.
How old do you have to be to have hypsarrhythmia?
Hypsarrhythmia rarely persists beyond the age of 24 months. Through the use of video EEG and continuous monitoring, five variants of the “classical” hypsarrhythmic pattern have been identified: Hypsarrhythmia with increased interhemispheric synchronization.